A case is presented of hydrops fetalis, polyhydramnios and intrauterine death diagnosed antenatally by ultrasound in which congenital cardiac rhabdomyoma was found at postmortem. Conditions associated with rhabdomyoma are briefly discussed.A case is presented of hydrops fetalis, polyhydramnios and intrauterine death diagnosed antenatally by ultrasound in which congenital cardiac rhabdomyoma was found at postmortem. Conditions associated with rhabdomyoma are briefly discussed.