The case of a 27 month old male with a congenital midline nasal dermoid cyst is presented, The child attended the Ear, Nose and Throat outpatient's department in July 1995, with an external midline nasal swelling, which had been present at birth and was noted to be gradually increasing in size, Magnetic resonance imaging (MRI) showed a central defect of the nasal bones, with a soft tissue mass at the upper part of the nasal bridge expanding the nasal septum, There was no radiological evidence of intracranial extension, The child had the nasal mass removed under general anesthesia, through an external rhinoplasty incision, Histopathology confirmed that the mass was a fully excised nasal dermoid cyst, Current investigation and management of this condition is discussed.